Esplenomegalia como signo de enfermedad lisosomal

  1. Luis Javier García Frade 1
  2. Ana Campano García 1
  3. J. Villarubia 1
  1. 1 Hospital Río Hortega de Valladolid
Revista:
Anales de la Real Academia de Medicina y Cirugía de Valladolid

ISSN: 0210-6523

Año de publicación: 2020

Número: 56

Páginas: 400-414

Tipo: Artículo

DOI: 10.24197/ARAMCV.56.2020.400-414 DIALNET GOOGLE SCHOLAR lock_openDialnet editor

Otras publicaciones en: Anales de la Real Academia de Medicina y Cirugía de Valladolid

Objetivos de desarrollo sostenible

Resumen

La estructura sana del bazo funciona como función hematopoyética para el período fetal; después, se convierte en un gran órgano linfoide, y también, es del sistema de filtro de células sanguíneas. La enfermedad de Gaucher es un extraño trastorno de almacenamiento lisosomal, muchos de ellos son hereditarios y multisistémicos. Hoy en día, setenta LSD han sido adoptados.

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