Esplenomegalia como signo de enfermedad lisosomal
- Luis Javier García Frade 1
- Ana Campano García 1
- J. Villarubia 1
- 1 Hospital Río Hortega de Valladolid
ISSN: 0210-6523
Year of publication: 2020
Issue: 56
Pages: 400-414
Type: Article
More publications in: Anales de la Real Academia de Medicina y Cirugía de Valladolid
Abstract
La estructura sana del bazo funciona como función hematopoyética para el período fetal; después, se convierte en un gran órgano linfoide, y también, es del sistema de filtro de células sanguíneas. La enfermedad de Gaucher es un extraño trastorno de almacenamiento lisosomal, muchos de ellos son hereditarios y multisistémicos. Hoy en día, setenta LSD han sido adoptados.
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